Cleidocranial Dysostosis – An Enigma Developmental Bones Anomaly

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A. O. Adebola Yusuf
A. Adeniyi
T. A. Oyedele
C. O. Akisanya


Cleidocranial Dysostosis, known also as Cleidocranial dysplasia, Mutational Dysostosis, Scheuthauer Marie-Sainton syndrome, is a rare condition which is characterized by delayed ossification of midline structures. Case study of the phenomenon has been reported here. Reports revealed that the classical association of a spectacular dental anarchy, with non-closure of cranial sutures, retention of deciduous teeth and delayed eruption of permanent denture and typical facies of underdevelopment raise strong suspicion of autosomal syndrome. The reviewed patient as a classic demonstration of cleidocranial dysostosis, succinctly represented the condition.

Cleidocranial dysostosis, mutational dysostosis, case study

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How to Cite
Yusuf, A. O., Adeniyi, A., Oyedele, T. A., & Akisanya, C. O. (2019). Cleidocranial Dysostosis – An Enigma Developmental Bones Anomaly. International Journal of Medical and Pharmaceutical Case Reports, 12(2), 1-8.
Case Report


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